Nicole Langenbach, Alexander Pfau, Michael Landthaler, Wilhelm Stolz
DOI: 10.1080/000155598443114

This is the first case in the literature describing naevi spili, café-au-lait spots and melanocytic naevi aggregated alongside Blaschko's lines. The pattern of melanocytic lesions in our patient is different from the congenital pigmentary syndromes and the segmental distribution of melanocytic naevi, the quadrant distribution of dysplastic naevi or the partial unilateral lentiginosis which here are shortly reviewed. The distribution may be a result of a somatic mutation occurring at an early stage of embryogenesis when neural structures had already been formed.